Systemic mastocytosis with hemophagocytic syndrome
نویسندگان
چکیده
منابع مشابه
Systemic mastocytosis and Sjögren's syndrome.
are more likely to have either contralateral or bilateral bony metastases, which is supported by the recent report' and our case. Fixation, possibly with radiotherapy and cryotherapy, is recommended for a lytic lesion in a weightbearing bone if the life expectancy is greater than three or four months.2 Metastases to periarticular foci are not uncommon, especially in the hip, shoulder, and knee,...
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circular macules, less than 1 cm in diameter, located on his trunk and extremities [Figure A]. Wheals and surrounding erythema developed in the lesions after rubbing (positive Darier sign). Laboratory analyses showed mild eosinophilia with an increased total tryptase level of 40 ng/ml. Densitometry was normal. With the strong clinical suspicion of cutaneous mastocytosis, a skin biopsy was perfo...
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Mastocytosis comprises a spectrum of disorders characterized by abnormal growth of mast cells (MS). Four entities are recognizable according to WHO classification. Association of systemic mastocytosis (SM) with a chronic myeloproliferative neoplasia (SM-AHNMD) is the second frequently category. Published descriptions of the clinicopathologic features of SM-AHNMD are largely limited to individua...
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Systemic mastocytosis (SM) is a condition associated with a clonal neoplastic proliferation of mast cells. Approximately 40% of patients with SM present with an associated clonal hematological non-mast cell lineage disorder. Patients presenting with SM-acute myeloid leukemia (AML) have the worst prognosis. We present a case of a 62-year-old woman who was diagnosed with SM-AML. After initial tre...
متن کاملHemophagocytic syndrome as the initial manifestation of systemic lupus erythematosus.
INTRODUCTION Hemophagocytic syndrome (HS) occurs in autoimmune diseases and belongs to the hemophagocytic lymphohistiocytosis group of diseases. This paper describes the features of 2 patients with systemic lupus erythematosus (SLE) who presented HS as the initial clinical manifestation. CLINICAL OBSERVATIONS Both patients had prolonged fever not associated to an infectious process and did no...
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ژورنال
عنوان ژورنال: Nihon Naika Gakkai Zasshi
سال: 2003
ISSN: 0021-5384,1883-2083
DOI: 10.2169/naika.92.874